- Selected Topics
- What is Deaf-Blindness
- Definitions of Deaf-Blindness
- Causes of Deaf-Blindness
- National Child Count & Demographics
- Communication Overview
- Early Communication
- Prelinguistic Communication
- Object Communication
- Symbolic Communication
- Sign Language
- Accessing the General Curriculum
- Auditory Training
- Calendar Systems
- Concept Development
- Daily Living Skills
- Environmental Considerations
- Harmonious Interactions
- Lilli Nielsen and Active Learning
- Orientation & Mobility
- Play & Recreation
- Social Interactions
- Tactile Strategies
- Universal Design for Learning
- van Dijk Approach
- Identification & Referral
- Early Intervention
- Assessment Overview
- Assessment Tools and Instruments
- Alternate Assessment
- Program Planning
- IEP Development
- IDEA (Individuals with Disabilities Education Act)
- Assistive Technology
- History of Deaf-Blind Education
- Self Determination
- Person Centered Planning
- Postsecondary Education
- Independent Living
- Customized Employment
- Sex Education
- Adult Services
- Intervener Services
- Support Service Provider
- Personnel Development & Training
- Interpreting for Deaf-Blind Individuals
- Interpreting for Deaf-Blind Individuals - Annotated Bibliography
- Training Resources
- Family Resources
- Personal Narratives - Family Stories
- Personal Narratives
- Art & Writing
- Cochlear Implants
- Functional Hearing
- Functional Vision
- Sensory Integration
- Central Auditory Processing Disorder/Auditory Neuropathy
- CHARGE Syndrome Webcasts and Presentations
- CHARGE Syndrome
- Congenital Rubella Syndrome (CRS)
- Cortical Visual Impairment
- Retinal Degenerative Disease
- Usher Syndrome
- Applications of Technology
- Research to Practice
- Topical Overviews
- Practice Perspectives
- Tools For TA
- Information Packets
- Deaf-Blind Perspectives
- Webinar Recordings
- NCDB eNews
- Archived Webinars
This is a partial list of materials on this topic available from the NCDB Catalog Database. If you have additional questions, please contact us via email: email@example.com
Audiologic Features of Norrie Disease --Halpin, Chris et. al . The Annals of otology, rhinology, and laryngology. 2005, 114 (7), 533-538. (2005)Norrie disease is an X-linked recessive disorder in which patients are born blind and develop sensory hearing loss in adolescence. The hearing loss associated with Norrie disease has been shown in a genetically altered knockout mouse to involve dysfunction of the stria vascularis; most other structures are preserved until the later stages of the disease. The objective of this study was to characterize the audiologic phenotype of Norrie disease for comparison with the pathophysiologic mechanism. The design combined two series of clinical audiologic evaluations, with special attention to speech intelligibility. The audiologic results for 12 affected individuals and 10 carriers show that patients with Norrie disease retain high speech intelligibility scores even when the threshold loss is severe. The cochlear mechanism-- failure of the stria vascularis-- accounts for some of the higher values in the wide distribution of speech scores in cases with similar pure tone audiograms.
Changes in Auditory Behaviors of Multiply Handicapped Children with Deafness after Hearing Aid Fitting --Kaga, Kimitaka; Shindo, Mitsuko; Tamai, Fumi; Tanaka, Yoshisato. ACTA OTO-LARYNGOLOGICA, vol. 127, #12, pp. 9-12. (2007)The subjects in this study consisted of 5 hearing-impaired infants with no other problems and 28 hearing-impaired children with multiple handicaps (vision status not reported). Behavioral audiometry and auditory brainstem responses were used to evaluate hearing impairment. The 5 hearing-impaired infants with no other problems underwent hearing aid fitting at approximately 1 year of age and the 28 hearing-impaired children with multiple handicaps underwent hearing aid fitting at various times from 1 to 5 years of age. The effects of their hearing aids were compared on the basis of auditory behavioral changes. The auditory behaviors of the hearing-impaired children with no other problems showed constant changes with age after hearing aid fitting. However, among the 28 hearing-impaired children with multiple handicaps, 17 showed improvement in auditory behaviors, 5 showed no improvement in auditory behaviors because of the associated severe motor and mental retardation, and epilepsy, and 6 were unable to adapt to wearing hearing aids. The authors recommend early diagnosis of deafness and the early fitting of hearing aids in multiply handicapped children even if a child's neurological or mental status is poor.
Cochlear Implantation in Children: Implications for the Primary Care Doctor --Goller, Yael, BS, RN, CPNP. JOURNAL OF THE AMERICAN ACADEMY OF NURSING PRACTITIONERS, vol. 18, 2006, pp. 397-408. (2006)The purpose of this article is to define hearing loss (HL), discuss the impact of HL on child development, and review the literature on cochlear implantation in children. The criteria for and the benefits and limitations of cochlear implantation in children, as well as the implications for the primary care provider with regard to children who have cochlear implants, are presented. A child's future development depends greatly on speech and language skills. Any type of HL can impact and may even hinder speech and language acquisition. It is therefore crucial to enforce early identification of HL. For severe to profoundly hearing-impaired children, cochlear implantation serves as an avenue for hearing and language development. Nurse practitioners ought to be up to date with criteria for and the benefits and risks of cochlear implantation. Health-related issues, such as vaccination, otitis media, and meningitis, must be assessed for and managed promptly.
Cochlear Implantations in Visually Impaired Patients --Takasaki, Kenji; Kanda, Yokihiko; Kumagami, Hidetaka; Yashida, Haruo; Yamamoto-Fukuda, Tomomi; Miyamoto, Ikue; Takahashi, Haruo. EUROPEAN ARCHIVES OF OTORHINOLARYNGOLOGY, (2007) 264: pp. 363-367. (2007)We retrospectively review the cases to evaluate the outcome of cochlear implantation (CI) in patients with severe-to-profound hearing loss and visual impairment (VI). Six adults with severe or profound hearing loss and significant VI underwent multichannel CI. Follow-up period ranged from 17 months to 7 years. Case history, etiology of visual and hearing loss, and benefit from CI were evaluated. To measure the outcomes, we selected the pure-tone thresholds with CI, the speech discrimination scores (SDS) using the Japanese video SDS system, the speech perception rates using the Japanese CD SDS system by monosyllable and word, and the open-set and closed sentence score using live voice. All the patients live happily after CI. There was no significant difference between the present six patients and the patients with profound hearing loss without VI in evaluations of hearing and quality of life. CI can play a significant rehabilitative role in patients with severe hearing loss and VI.
Deaf Children With Severe Multiple Disabilities: Etiologies, Intervention, and Assessment / van Dijk, Rick; Nelson, Catherine; Postma, Albert; van Dijk, Jan. -- Oxford Handbook of Deaf Studies, Language, and Education, Vol. 2. Marc Marschark & Patricia Elizabeth Spencer (Eds.), pp. 172-191. OxfordUniversity Press: (2010)
The emphasis of this book chapter is on individuals who are deaf or hard of hearing and have additional severe disabilities, including intellectual disabilities, autism, or deaf-blindness. Their disabilities can be due to many factors including genetic syndromes; problems that occur before, during, or slightly after birth; or infections such as meningitis or injuries, such as brain injury, that are acquired later in life. This chapter describes several of the major causative factors and presents important evidence-based practices that have the potential to enhance the communication, education, and quality of life of this population of individuals.
Dual Sensory Loss: Overview of Problems, Visual Assessment, and Rehabilitation --Brabyn, John A., PhD Schneck, Marilyn E., PhD Haegerstrom-Portnoy, Gunilla, OD, PhD Lott, Lori A., PhD. TRENDS IN AMPLIFICATION, December 2007,Vol. 11, No. 4, pp. 219-226. (2007)This article provides an overview of some of the problems and possible solutions surrounding the neglected issue of combined vision and hearing deficits. The subject is treated by considering each subpopulation, ranging from those who have no residual vision or hearing to those with mild coexisting vision and hearing losses. An attempt is made to relate the different types of visual deficit to the likely problems encountered in real-life activities, such as communication and travel, among individuals who also have a hearing impairment. The assessment and appropriate referral of patients with these combined deficits is discussed, including the interpretation of visual test results and the importance of factors other than standard visual acuity. Speculation is offered on potential strategies and solutions for rehabilitation as well as the need for future research and improvements in service delivery.
Effect of Dual Sensory Loss on Auditory Localization: Implications for Intervention --Simon, Helen J., PhD; Levitt, Harry, PhD. TRENDS IN AMPLIFICATION, December 2007, Vol. 11, No. 4, pp. 259-272. (2007)Our sensory systems are remarkable in several respects. They are extremely sensitive, they each perform more than one function, and they interact in a complementary way, thereby providing a high degree of redundancy that is particularly helpful should one or more sensory systems be impaired. In this article, the problem of dual hearing and vision loss is addressed. A brief description is provided on the use of auditory cues in vision loss, the use of visual cues in hearing loss, and the additional difficulties encountered when both sensory systems are impaired. A major focus of this article is the use of sound localization by normal hearing, hearing impaired, and blind individuals and the special problem of sound localization in people with dual sensory loss.
Have GPS, Will Travel --Spiers, Elizabeth. THE DEAF-BLIND AMERICAN, vol. 48, #2, Winter 2009, pp. 26-29
This article is about Joe Jammer, who is hard of hearing and blind. At the time of the article he was a student at Helen Keller National Center in New York. He obtained his Braille Sense Plus and GPS add-on through the California Department of Vocational Rehabilitation and received training through the Helen Keller Technology Department. His Braille Sense has email, internet service, word processing, and an address book. He is still learning these functions and uses the Braille Sense now mainly for the GPS. Mr. Jammer's Braille Sense Plus also has an LCD display so that sighted people who don't know braille can communicate with him if needed, and vice versa. He now can travel to a restaurant of his choice and know exactly how to go. He can take a cab anywhere and tell the driver the best and quickest way to his destination by using his GPS.
Hearing Assistive Technology Considerations for Older Individuals With Dual Sensory Loss --Kricos, Patricia B. TRENDS IN AMPLIFICATION, December 2007 Vol. 11, No. 4, pp. 273-279. (2007)This article focuses on the current state of the science related to audiologic rehabilitation of individuals with dual sensory impairment, with an emphasis on considerations for provision of appropriate hearing assistive technology for this population. A substantial increase in the number of older adults is predicted in the coming years, many of whom will have significant age-related impairments in hearing and vision. Thus, hearing care professionals will be called on increasingly to attend to the special needs of people with dual sensory impairment to ensure maximal quality of life and independence for these individuals. Access to sound is critical for individuals who live with compromises in both vision and hearing. Hearing assistive technology may improve not only their speech perception but also their connection and orientation to the environment, as well as enable greater mobility. Thus, the audiologist's provision of appropriate and carefully selected hearing assistive technology may contribute dramatically to the quality of life of the individual with dual sensory loss. Prefitting, fitting, and postfitting considerations in providing hearing aids and other assistive technology to individuals with dual sensory impairment are reviewed.
Hearing, Hearing Aids and Implants in CHARGE Syndrome --Thelin, James W. Miami Beach, FL: 7th International CHARGE Syndrome Conference, July 22nd - July 24th, 2005, Miami Beach, Florida. (2005)This paper is divided in three sections, hearing, hearing aids and implants. Each section has a section called personal factors which has a list of questions that help personalize the information. Each section also has a list of factors that discuss specific CHARGE related things relating to hearing, hearing aids or implants.
Identification of Congenital Deafblindness --Andersen, Karen; Rodbroe, Inger. The Danish Resource Centre on Congenital Deafblindness. (2006)This publication consists of the following booklets: (2A) Examination of Vision - Suggestions for Medical and Functional Assessments; (2B) Examination of Hearing - Suggestions for Medical and Functional Assessments; (2C) Examination of the Tactile Sense - Suggestions for Medical and Functional Assessments; and (3) Examination and Observation - Assessment of the Functioning of the Senses in Interaction and Communication.
Implications of Deafblindness on Visual Assessment Procedures : Considerations for Audiologists, Ophthalmologists, and Interpreters --Hyvarinen, Lea. TRENDS IN AMPLIFICATION, vol. 11, #4, December 2007, pp. 227-232: (2007)This article describes strategies that ophthalmologists and audiologists can use when assessing the vision or hearing of individuals who are deaf-blind. It also describe how these professionals can work with interpreters during the assessment process.
Ophthalmologic Disorders in Children With Syndromic and Nonsyndromic Hearin Loss -- Johnston, Douglas R.; Curry, Joseph M.; Newborough, Brian; Morlet, Thierry; Bartoshesky, Louis; Lehnam, Sharon; Ennis, Sara; O'Reilly, Robert C. ARCHIVES OF OTOLARYNGOLOGY HEAD NECK SURGERY, 136(3), March 2010, 277-280 (2010)
The goal of this study was to identify the rate of eye disorders in 77 children with syndromic and nonsyndromic congenital sensorineural hearing loss (SNHL), but with no other history of ophthalmologic disease. Children with well-defined risk factors for ophthalmologic and auditory impairment (e.g., prematurity, congenital infections) were excluded. The method was a retrospective review of the medical records of children with congenital SNHL seen in a department of otolaryngology at a pediatric hospital over a 5-year period who received ophthalmologic and genetic evaluations. A clinically significant ophthalmologic disorder was identified in 25 of 77 (32%). When children with multisystem genetic disorders known to be related visual loss were excluded, the rate fell to 23% (12 of 53 without, as compared to 13 of 24 with, a multisystem disorder). Although this rate of vision loss is lower than the rate for children with systemic disorders, it is still 2 to 3 times that of the general pediatric population. This indicates a need for ophthalmologic evaluation in children with apparently isolated SNHL. The children with multisystem conditions had a variety of conditions including CHARGE syndrome (2), Down syndrome (2), Waardenburg syndrome (2). None had Usher syndrome. The degree of SNHL was not predictive of eye or vision abnormalities. The most common types of problems were motility disorders (inward or outward eye deviation), refractive disorders (near-sightedness, far-sightedness, anisometropia, astigmatism), structural disorders (iris heterochromia, coloboma, cataracts), and neuro-ophthalmologic disorders (optic atrophy, nystagmus, optic disc anomaly).
Ophthalmologic Findings in Children With Sensorineural Hearing Loss --Sharma, Arun; Ruscetta, Melissa N.; Chi, David H. ARCHIVES OF OTOLARYNGOLOGY HEAD NECK SURGERY, vol. 135, #2, February 2009, pp. 119-123 (2009)
The purpose of this study was to determine the prevalence of refractive and nonrefractive ophthalmologic abnormalities in children with sensorineural hearing loss (SNHL) and to evaluate the overall utility of routine ophthalmological examination in children with SNHL. The design was a retrospective analysis of ophthalmologic findings in the medical records children 18 years and younger with SNHL seen at Children's Hospital of Pittsburgh between November 2000 and June 2007. Records were reviewed for 226 children (mean age at diagnosis was 37 months). Of these, 49 (21.7%) had an ophthalmologic abnormality. Refractive errors (e.g., myopia, hyperopia, astigmatism) were present in 23 (10.2%). Nonrefractive conditions (e.g., strabismus, retinitis pigmentosa) were present in 29 (12.8%). The prevalence of ophthalmologic abnormalities was not significantly different between children whose conditions were diagnosed on the basis of newborn hearing screening and other children.
Prevalence of Combined Vision Impairment and Hearing Loss: The Importance of Comorbidity Studies --Slaets, JP. Nederlands Tijdschrift Voor Geneeskunde [Ned Tijdschr Geneeskd] 2007 Jun 30; Vol. 151 (26), pp.1451-3. (2007)
Eight recent Dutch studies were analyzed to determine the prevalence of dual sensory impairment: impaired vision and hearing loss. The study showed a strong increase in the prevalence of dual sensory impairment above the age of 85. In the general population, there was a 10-fold increase in prevalence between 65-80 years of age (0.5%) and 85 years and older (6%). For all age categories, the prevalence was even higher in nursing homes (7-25%) and among mentally retarded persons (6-13%). Visual impairment and hearing loss have negative effects on well-being because of the impact on resources and because of an increase in dependency and stress. Other forms of coomobidity with vision impairment or hearing loss, such as combinations with cardiovascular or psychiatric diseases, are even more important for healthcare than dual sensory impairment. The influence of comorbidity on functioning and well-being is still poorly investigated and there is a lack of empirical evidence concerning the effect of treatment in comorbid conditions.
Sensory Perspectives DVD-- SKI-HI Institute, Utah State University -- (2003)
This 2 set DVD provides information and simulations regarding hearing loss, vision loss, and deaf-blindness. Disk 1 contains 2 sections, one on vision loss and one on hearing loss. The section on vision loss includes an introduction to vision, and explanations and simulations of different types of acuity loss, field loss, conditions that may cause combined field and acuity loss, contrast sensitivity, processing problems, and oculomotor problems. The hearing loss section includes an introduction to hearing, hearing loss information, hearing loss simulations, and environmental issues. Disk 2 focus on combined vision and hearing loss. It includes an introduction to deafblindness, and sections on deafblindness and learning, communication, and social and emotional development. It also has a number of simulations where the user can combine a specific type of vision loss (e.g., acuity loss, field loss, or cortical visual impairment) with a specific frequency level of hearing loss or central auditory processing disorder. There is an option to view the DVD with Spanish and also with closed captioning if viewing with a captioning decoder box or a television with a closed captioning decoder. Available from HOPE, Inc., 1856 North 1200 East, North Logan, UT 84321. Phone: 435-245-2888. E-mail: firstname.lastname@example.org. Publisher's web site: http://www.hopepubl.com
What to Expect at a Child's Hook-up --Cochlear Limited. CO: Video, 27 minutes, October 2001. (2005) This short video discusses strategies on how an implant works, the initial hook up, fitting the headset, programming the processor, selecting the speech coding along with the first hearing experiences and expectations of how the hook up works.